FARS includes neurological signs that specifically reflect neural substrates
affected in FRDA. Based on a neurological examination bulbar, upper limb, lower
limb, peripheral nerve, and upright stability/gait functions are assessed.
Further, a functional staging and activities of daily living (ADL) assessment
are incorporated. The scales are supplemented by quantitative performance
measures including 8m walk at maximum speed (8MW), the 9-hole peg test (9HPT),
PATA rate and low-contrast letter acuity.
Subramony SH, May W, Lynch D, Gomez C, Fischbeck K et al. Measuring
Friedreich ataxia: Interrater reliability of a neurologic rating scale.
Lynch DR, Farmer JM, Tsou AY, Perlman S, Subramony
SH et al. Measuring Friedreich ataxia: complementary features of examination and
performance measures. Neurology 2006; 66:1711-1716.
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